Lymphangiomatosis is rare in both adults and children. We present an 11 year old boy with right chylothorax. The formation of chylothorax was a result of diffuse lymphangioma in the mediastinum spreading to the pleura. In addition, this patient suffered from cystic bone lesions.
The child was finally diagnosed as having lymphangiomatosis based on pleural biopsy and bone lesions found on CTs and MRI. He was treated by pleurectomy and propranol as well as control of anemia and infection.
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